Monogenic diabetes mellitus is a heterogeneous group of single-gene disorders that lead to diabetes. Maturity-Onset Diabetes of the Young is the most common type of monogenic diabetes, usually inherited as autosomal dominant or recessive. The prevalence of this type of diabetes starting at a young age is extremely rare. The present study is a report of an eleven year old boy with MODY. The patient is currently on a diet and MDI diet And his illness was in control.